What Is Eagle-Barrett Syndrome?
Eagle - Barrett Syndrome which is also known by the name of Prune Belly Syndrome is an extremely rare pathological condition in which the affected individual has partial or gross absence of the abdominal muscles and the stomach is underdeveloped .
The affected individual also has undescended ball along with multiple abnormalities of the urinary tract . Some of the urinary abnormalities admit unnatural turnout of the tubes which carries urine to the ureter . There is also unnatural accruement of the water in the ureters or the kidneys or a backflow of the urine from the bladder back into the ureters .
Some of the other abnormality associated with Eagle - Barrett Syndrome include developing lung and nonadaptive kidney . The reason as to why this shape occurs is not yet know but enquiry is ongoing so as to discover a causa for the development of Eagle - Barrett Syndrome .
What Are The Causes Of Eagle-Barrett Syndrome?
The root cause for Eagle - Barrett Syndrome is not yet known but there have been many suggestion put forrad by various investigator that could potentially be the cause of Eagle - Barrett Syndrome .
One hypothesis suggest that Eagle - Barrett Syndrome may result from bladder mental defectiveness during fetal developing have this condition . The reason behind this is stated as when there is unnatural accumulation of urine within the ureter and the bladder there is enlargement of the vesica leading to atrophy of the abdominal muscles .
This urinary retentivity is also conceive to be the cause of undescended bollock . The 2d theory for the development of Eagle - Barrett Syndrome suggests that developing abdominal muscles are the cause of Eagle - Barrett Syndrome .
The third and final theory suggests that a nervous system defect is a possible cause for the irregularity in the abdominal muscles resulting in the maturation of Eagle - Barrett Syndrome .
These theories put together various observation made by researchers which may luff towards a causal agent of this condition but there is no literal validation that any one of these above mentioned theories are in reality the cause of Eagle - Barrett Syndrome .
What Are The Symptoms Of Eagle-Barrett Syndrome?
The primary presenting feature of Eagle - Barrett Syndrome is complete or fond absence of abdominal muscles or developing abdominal sinew which can be detected at the clock time of birth which gives the abdomen a prune like appearance and hence this precondition is also called as Prune Belly Syndrome .
The thickness of the sinew above the vesica is at a minimum in this condition . The abdomen appears abnormally large and is lax . The bladder is also enlarged in fount of Eagle - Barrett Syndrome .
The bladder cervix is usually close up which causes vesica and urinary retentiveness . The vesica and ureter possible action may also be quite narrow or in some grammatical case altogether closed .
There is also kidney and ureteral obstruction . In some case , the affected individual may also have renal cysts as a result of Eagle - Barrett Syndrome . The affected individual may also have hematuria or pyuria signaling to the possibility of an infection . Undescended ball are also one of the features of Eagle - Barrett Syndrome .
How Is Eagle-Barrett Syndrome Diagnosed?
The diagnosis of Eagle - Barrett Syndrome is usually made shortly after the birth of a shaver . The characteristic features of the condition with an abnormally great abdomen may be a pointer towards this stipulation .
Once a diagnosis of Eagle - Barrett Syndrome is suspected radiographic studies in the cast of MRI or an ultrasound of the belly will clearly show abnormalities of the muscle of the abdomen confirming the diagnosing of Eagle - Barrett Syndrome .
How Is Eagle-Barrett Syndrome Treated?
The treatment for Eagle - Barrett Syndrome is mostly symptomatic and count on the severity of the shape . In some wicked cases , operative treatment will have to be done to correct the abnormalities that are present as a outcome of Eagle - Barrett Syndrome .
Some of the procedures that may be done is creating an opening in the bladder through the abdomen thus getting rid of the urinary obstructer and assist in voiding . operative subprogram may also be expect to right the undescended testicle and correct the abnormalcy .
In some cases more complicated surgical procedures such as vesica reconstruction , widening of the urethra , and detrusor augmentation have been quite successful in treating the symptoms of Eagle - Barrett Syndrome . In extremely rare grammatical case , kidney transplantation has been required to handle Eagle - Barrett Syndrome .
