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West syndrome also known as West ’s Syndrome is a rare epileptic disorder see in infants . This syndrome was named after William James West who was an English doc and a sawbones . He had observe this form of epilepsy in his son , James E. West , when he was around four month old . He named the seizures experienced by his son at that clock time as “ Salaam tic . ” West ’s Syndrome is also eff as Infantile Epileptic Encephalopathy , Generalized Flexion Epilepsy , Infantile Myoclonic Encephalopathy , Massive Myoclonia , Jackknife Convulsions and Salaam Spasms .
West syndrome consists of a triad of infantile muscle spasm , genial retardation and a pathognomonic EEG pattern recognize as hypsarrhythmia . However , the international definition of this term require only two of these three elements .
West ’s syndrome is age - related and commonly appears when the child is aged between three and twelve months . It most usually manifests around the fifth month . There are different causes for this condition ( “ polyetiology ” ) ; the common suit being an constitutional brain dysfunction , which can be antenatal , perinatal or postnatal .
According to statistics , boys are more prostrate to be strike by this condition than girls . Commonly the muscle spasm produce for the first clock time when the child is between three and twelve months of age . seldom , muscle spasm can occur in the first two calendar month of the child ’s life or when the tike is between two to four years old .
Causes of West’s Syndrome
The precise cause or the bio - chemical chemical mechanism , which run to West ’s syndrome is not clear . It is thought to occur due to a malfunction in the social function of a neurotransmitter or a malfunction in the management of the GABA transmission physical process . Other movement think to be responsible for include over - product of the corticotropin - releasing hormone ( CRH ) . It is quite potential that more than one cause is behind it .
If the suit of west ’s syndrome is identify , then the condition is allege to be ” symptomatic ” West ’s syndrome because the attacks occur as a symptom of some other problem . Any case of brain impairment can be related and are divide into antenatal , perinatal , and post - natal . Given below is the list of conditions , which can cause West ’s ’ syndrome :
About 1/3 of the children have constituent disorderliness of the genius , which let in the followers :
extra possible causes of West ’s ’ syndrome admit :
Signs & Symptoms of West’s Syndrome
“ Infantile Spasms ” is a mathematical group which make up of three categories of the epileptic capture see in baby having West ’s syndrome . Commonly the shaver with West ’s syndrome experience a tierce of plan of attack character . These three type often take place simultaneously ; however , they can also occur individually .
Investigations for West’s Syndrome
Treatment for West’s Syndrome
Prognosis & Life Expectancy for West’s Syndrome
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